LAM

CT scan shows something like this

- Regular and rounded cystic lesions

- This is lymphangioleiomyomatosis

Learning points:

1) Recurrent pneumothorax in a lady in child bearing age - consider LAM

2) LAM can have pleural effusion ( chylous effusion )

3) Ddx of cystic lung patterns are short : consider LAM vs Langerhans cell histiocytosis vs pneumatoceles, other diseases include lymphocytic interstitial pneumonia

Langerhans cell histiocytosis is

1) Upper lobe predominance

2) Irregular cystic lesions with weird shaped